18 years old boy from Sudan presented with breathlessness since 5-6 months and cramps in lower limbs.He also had history of haemorrhagic stroke with basal ganglion bleed 6 months back. He was investigated in MaxCure Hospital, Madhapur. CT scan showed gap between the ascending and descending thoracic aorta,ECHO showed heart pumping-
Dr Pramod Reddy Kandakure has performed this rare surgery in MaxCure Hospital, Hyderabad.He used an artificial tube to join two parts of aorta.Boy recovered well after surgery. Nearly all patients with interrupted aortic arch present in the first 2 weeks of life. This boy was diagnosed late due to lack of facilities in his own country. Ideally his surgery should have been done before one year of age. Dr Pramod has done advanced fellowship in aortic surgery in UK.
Interrupted aortic arch is a very rare heart defect (affecting 3 per million live births) in which the aorta is not completely developed. Interrupted aortic arch (IAA) is the absence or discontinuation of a portion of the aortic arch.Interrupted aortic arch is thought to be a result of faulty development of the aortic arch system during the fifth to seventh week of fetal development.In patients with interrupted aortic arch, oxygen-rich blood from the left side of the heart is not able to reach all areas of the body because of the defect in the aortic arch.In a child with interrupted aortic arch, the PDA provides a critical alternate way to get adequate blood flow to the lower body.
In most cases of interrupted aortic arch (IAA), with good surgical repair, the prognosis is excellent.